Abstract
Backgrounds and purpose - To correlate the extent of the leptomeningeal angiomatosis with clinical features in Sturge-Weber syndrome (SWS). Methods - The study group consisted of 86 consecutive patients aged two months to 56 (mean 7.9±10.3) years with SWS and epilepsy. Clinical and MRI data were analyzed. Results - Based on the extent of leptomeningeal angiomatosis, patients were divided into two subgroups: 43 patients had hemispheric angiomatosis and atrophy, whereas, another 43 had focal involvement. Nine of the 43 hemispherial patients (10%) showed bilateral involvement: all of these bilateral cases demonstrated dominance in a single side with hemispheric leptomeningeal angiomatosis and contralateral focal extension. Hemispheric and focal subgroups were clinically different. Patients with hemispheric SWS were younger at the age of epilepsy onset (p
Original language | English |
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Pages (from-to) | 53-57 |
Number of pages | 5 |
Journal | Ideggyógyászati szemle |
Volume | 66 |
Issue number | 1-2 |
Publication status | Published - jan. 30 2013 |
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ASJC Scopus subject areas
- Clinical Neurology
- Neurology
Cite this
Sturge-Weber syndrome : Clinical and radiological correlates in 86 patients. / Fogarasi, A.; Loddenkemper, Tobias; Mellado, Cecilia; Tuxhorn, Ingrid; Evers, Georg; Sarco, Dean; Burgess, Richard C.; Halász, P.; Barsi, P.; Gyorsok, Zsuzsanna; Gyimesi, Csilla; Kóbor, Jeno; Siegler, Zsuzsanna; Janszky, J.; Jakus, R.; Rásonyi, G.; Ebner, Alois; Woermann, Friedrich G.; Sahin, Mustafa.
In: Ideggyógyászati szemle, Vol. 66, No. 1-2, 30.01.2013, p. 53-57.Research output: Article
}
TY - JOUR
T1 - Sturge-Weber syndrome
T2 - Clinical and radiological correlates in 86 patients
AU - Fogarasi, A.
AU - Loddenkemper, Tobias
AU - Mellado, Cecilia
AU - Tuxhorn, Ingrid
AU - Evers, Georg
AU - Sarco, Dean
AU - Burgess, Richard C.
AU - Halász, P.
AU - Barsi, P.
AU - Gyorsok, Zsuzsanna
AU - Gyimesi, Csilla
AU - Kóbor, Jeno
AU - Siegler, Zsuzsanna
AU - Janszky, J.
AU - Jakus, R.
AU - Rásonyi, G.
AU - Ebner, Alois
AU - Woermann, Friedrich G.
AU - Sahin, Mustafa
PY - 2013/1/30
Y1 - 2013/1/30
N2 - Backgrounds and purpose - To correlate the extent of the leptomeningeal angiomatosis with clinical features in Sturge-Weber syndrome (SWS). Methods - The study group consisted of 86 consecutive patients aged two months to 56 (mean 7.9±10.3) years with SWS and epilepsy. Clinical and MRI data were analyzed. Results - Based on the extent of leptomeningeal angiomatosis, patients were divided into two subgroups: 43 patients had hemispheric angiomatosis and atrophy, whereas, another 43 had focal involvement. Nine of the 43 hemispherial patients (10%) showed bilateral involvement: all of these bilateral cases demonstrated dominance in a single side with hemispheric leptomeningeal angiomatosis and contralateral focal extension. Hemispheric and focal subgroups were clinically different. Patients with hemispheric SWS were younger at the age of epilepsy onset (p
AB - Backgrounds and purpose - To correlate the extent of the leptomeningeal angiomatosis with clinical features in Sturge-Weber syndrome (SWS). Methods - The study group consisted of 86 consecutive patients aged two months to 56 (mean 7.9±10.3) years with SWS and epilepsy. Clinical and MRI data were analyzed. Results - Based on the extent of leptomeningeal angiomatosis, patients were divided into two subgroups: 43 patients had hemispheric angiomatosis and atrophy, whereas, another 43 had focal involvement. Nine of the 43 hemispherial patients (10%) showed bilateral involvement: all of these bilateral cases demonstrated dominance in a single side with hemispheric leptomeningeal angiomatosis and contralateral focal extension. Hemispheric and focal subgroups were clinically different. Patients with hemispheric SWS were younger at the age of epilepsy onset (p
KW - Age
KW - Epilepsy
KW - MRI
KW - Sturge-Weber syndrome
UR - http://www.scopus.com/inward/record.url?scp=84875531608&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=84875531608&partnerID=8YFLogxK
M3 - Article
C2 - 23607230
AN - SCOPUS:84875531608
VL - 66
SP - 53
EP - 57
JO - Ideggyogyaszati Szemle
JF - Ideggyogyaszati Szemle
SN - 0019-1442
IS - 1-2
ER -