Sturge-Weber syndrome: Clinical and radiological correlates in 86 patients

A. Fogarasi, Tobias Loddenkemper, Cecilia Mellado, Ingrid Tuxhorn, Georg Evers, Dean Sarco, Richard C. Burgess, P. Halász, P. Barsi, Zsuzsanna Gyorsok, Csilla Gyimesi, Jeno Kóbor, Zsuzsanna Siegler, J. Janszky, R. Jakus, G. Rásonyi, Alois Ebner, Friedrich G. Woermann, Mustafa Sahin

Research output: Article

3 Citations (Scopus)

Abstract

Backgrounds and purpose - To correlate the extent of the leptomeningeal angiomatosis with clinical features in Sturge-Weber syndrome (SWS). Methods - The study group consisted of 86 consecutive patients aged two months to 56 (mean 7.9±10.3) years with SWS and epilepsy. Clinical and MRI data were analyzed. Results - Based on the extent of leptomeningeal angiomatosis, patients were divided into two subgroups: 43 patients had hemispheric angiomatosis and atrophy, whereas, another 43 had focal involvement. Nine of the 43 hemispherial patients (10%) showed bilateral involvement: all of these bilateral cases demonstrated dominance in a single side with hemispheric leptomeningeal angiomatosis and contralateral focal extension. Hemispheric and focal subgroups were clinically different. Patients with hemispheric SWS were younger at the age of epilepsy onset (p

Original languageEnglish
Pages (from-to)53-57
Number of pages5
JournalIdeggyógyászati szemle
Volume66
Issue number1-2
Publication statusPublished - jan. 30 2013

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Sturge-Weber Syndrome
Angiomatosis
Epilepsy
Age of Onset
Atrophy

ASJC Scopus subject areas

  • Clinical Neurology
  • Neurology

Cite this

Fogarasi, A., Loddenkemper, T., Mellado, C., Tuxhorn, I., Evers, G., Sarco, D., ... Sahin, M. (2013). Sturge-Weber syndrome: Clinical and radiological correlates in 86 patients. Ideggyógyászati szemle, 66(1-2), 53-57.

Sturge-Weber syndrome : Clinical and radiological correlates in 86 patients. / Fogarasi, A.; Loddenkemper, Tobias; Mellado, Cecilia; Tuxhorn, Ingrid; Evers, Georg; Sarco, Dean; Burgess, Richard C.; Halász, P.; Barsi, P.; Gyorsok, Zsuzsanna; Gyimesi, Csilla; Kóbor, Jeno; Siegler, Zsuzsanna; Janszky, J.; Jakus, R.; Rásonyi, G.; Ebner, Alois; Woermann, Friedrich G.; Sahin, Mustafa.

In: Ideggyógyászati szemle, Vol. 66, No. 1-2, 30.01.2013, p. 53-57.

Research output: Article

Fogarasi, A, Loddenkemper, T, Mellado, C, Tuxhorn, I, Evers, G, Sarco, D, Burgess, RC, Halász, P, Barsi, P, Gyorsok, Z, Gyimesi, C, Kóbor, J, Siegler, Z, Janszky, J, Jakus, R, Rásonyi, G, Ebner, A, Woermann, FG & Sahin, M 2013, 'Sturge-Weber syndrome: Clinical and radiological correlates in 86 patients', Ideggyógyászati szemle, vol. 66, no. 1-2, pp. 53-57.
Fogarasi A, Loddenkemper T, Mellado C, Tuxhorn I, Evers G, Sarco D et al. Sturge-Weber syndrome: Clinical and radiological correlates in 86 patients. Ideggyógyászati szemle. 2013 jan. 30;66(1-2):53-57.
Fogarasi, A. ; Loddenkemper, Tobias ; Mellado, Cecilia ; Tuxhorn, Ingrid ; Evers, Georg ; Sarco, Dean ; Burgess, Richard C. ; Halász, P. ; Barsi, P. ; Gyorsok, Zsuzsanna ; Gyimesi, Csilla ; Kóbor, Jeno ; Siegler, Zsuzsanna ; Janszky, J. ; Jakus, R. ; Rásonyi, G. ; Ebner, Alois ; Woermann, Friedrich G. ; Sahin, Mustafa. / Sturge-Weber syndrome : Clinical and radiological correlates in 86 patients. In: Ideggyógyászati szemle. 2013 ; Vol. 66, No. 1-2. pp. 53-57.
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