Thrombotic thrombocytopenic purpura, moschcowitz syndrome

J. Müller, J. Czinyéri, I. Sasvári, M. Garami, G. Kovács

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Abstract

The authors present a case of a 16-year-old boy, who was referred to the hospital due to thrombocytopenia, anemia, proteinuria and hyperbilirubinemia. Based on the clinical picture and the laboratory data, thrombotic thrombocytopenic purpura (TTP) was diagnosed. The adequate therapy was immediately started. TTP is quite a rare entity. The etiology and the pathogenesis are not well defined. The authors summarize the different pathomechanisms, which may play a role in the development of TTP. Similarity to the hemolytic uremic syndrome (HUS), therapeutic possibilities, prognosis and the outcome are also discussed. The importance of the early diagnosis of TTP in childhood, and life-saving effect of the adequate treatment are emphasized.

Original languageEnglish
Pages (from-to)144-149
Number of pages6
JournalInternational Pediatrics
Volume16
Issue number3
Publication statusPublished - Jan 1 2001

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Keywords

  • Plasma exchange (PEX)
  • Plasmapheresis
  • Thrombotic thrombocytopenic purpura (TTP)

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

Cite this

Müller, J., Czinyéri, J., Sasvári, I., Garami, M., & Kovács, G. (2001). Thrombotic thrombocytopenic purpura, moschcowitz syndrome. International Pediatrics, 16(3), 144-149.