Miyazaki Syndrome due to Ventriculoperitoneal Shunt Treatment

Anita Kovács, Tamás Németh, Angéla Csomor, Tímea Novák, Ferenc Kövér, E. Vörös

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

Background: The signs and pathomechanism of Miyazaki syndrome is presented through the case of a young female patient. Case Description: The 33-year-old patient had undergone placement of a ventriculoperitoneal shunt with a pressure-adjustable valve for communicating hydrocephalus years before presenting to our department with the complaints of constant headache and unsteady gait. On the basis of the clinical picture and her history, plain and contrast-enhanced cranial and whole spine magnetic resonance imaging and magnetic resonance angiography examinations were performed, with the scans revealing signs indicative of cerebrospinal fluid hypotension typical of Miyazaki syndrome. Conclusion: The article discusses the available literature suggesting the underlying cause in such cases to be the dysfunction of the Starling resistor mechanism due to an improperly adjusted ventriculoperitoneal shunt, which results in excessive cerebrospinal fluid loss accompanied by consequent cerebral venous overflow with vertebral venous engorgement and compressive cervical myelopathy.

Original languageEnglish
Pages (from-to)29-34
Number of pages6
JournalWorld Neurosurgery
Volume116
DOIs
Publication statusPublished - Aug 1 2018

Fingerprint

Ventriculoperitoneal Shunt
Cerebrospinal Fluid
Neurologic Gait Disorders
Starlings
Spinal Cord Compression
Magnetic Resonance Angiography
Hyperemia
Hydrocephalus
Hypotension
Headache
Spine
History
Magnetic Resonance Imaging
Pressure
Therapeutics

Keywords

  • Cerebrospinal fluid hypotension
  • Miyazaki syndrome
  • Overshunting-associated myelopathy
  • Ventriculomegaly
  • Ventriculoperitoneal shunt

ASJC Scopus subject areas

  • Surgery
  • Clinical Neurology

Cite this

Miyazaki Syndrome due to Ventriculoperitoneal Shunt Treatment. / Kovács, Anita; Németh, Tamás; Csomor, Angéla; Novák, Tímea; Kövér, Ferenc; Vörös, E.

In: World Neurosurgery, Vol. 116, 01.08.2018, p. 29-34.

Research output: Contribution to journalArticle

Kovács, A, Németh, T, Csomor, A, Novák, T, Kövér, F & Vörös, E 2018, 'Miyazaki Syndrome due to Ventriculoperitoneal Shunt Treatment', World Neurosurgery, vol. 116, pp. 29-34. https://doi.org/10.1016/j.wneu.2018.05.032
Kovács, Anita ; Németh, Tamás ; Csomor, Angéla ; Novák, Tímea ; Kövér, Ferenc ; Vörös, E. / Miyazaki Syndrome due to Ventriculoperitoneal Shunt Treatment. In: World Neurosurgery. 2018 ; Vol. 116. pp. 29-34.
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