Magnetic resonance studies in management of adult cases with Bland-White-Garland syndrome

A. Komócsi, T. Símor, Levente Tóth, Sándor Szabados, Ferenc Mágel, Tünde Pintér, D. Aradi, Attila Kónyi, I. Horváth, L. Papp

Research output: Contribution to journalArticle

9 Citations (Scopus)

Abstract

Bland-White-Garland syndrome (BWG) is a rare congenital anomaly that is predominantly discovered in infancy. BWG is characterized by an anomalous origin of the left coronary trunk from the pulmonary artery that produces a coronary steal phenomenon, left-to-right shunt, and thus an abnormal left ventricular perfusion. The latter may induce myocardial necrosis, left ventricular dysfunction and commonly associated with mitral regurgitation. Despite its high mortality without surgical repair in infancy, several cases were reported to reach adulthood. In some patients, however, BWG was revealed only in older age, and may cause mild symptoms. Recent developments in cardiovascular MRI enable the determination of heart function, viability and perfusion with high resolution. We present three middle-aged female BWG cases indicating that MRI studies may give further insight into the therapeutic decision making in this age-group.

Original languageEnglish
JournalInternational Journal of Cardiology
Volume123
Issue number1
DOIs
Publication statusPublished - Dec 15 2007

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Bland White Garland Syndrome
Case Management
Magnetic Resonance Spectroscopy
Perfusion
Mitral Valve Insufficiency
Left Ventricular Dysfunction
Pulmonary Artery
Decision Making
Necrosis
Age Groups
Mortality

Keywords

  • Bland-White-Garland syndrome
  • Cardiac MR

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

Cite this

Magnetic resonance studies in management of adult cases with Bland-White-Garland syndrome. / Komócsi, A.; Símor, T.; Tóth, Levente; Szabados, Sándor; Mágel, Ferenc; Pintér, Tünde; Aradi, D.; Kónyi, Attila; Horváth, I.; Papp, L.

In: International Journal of Cardiology, Vol. 123, No. 1, 15.12.2007.

Research output: Contribution to journalArticle

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AU - Mágel, Ferenc

AU - Pintér, Tünde

AU - Aradi, D.

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