Intravascularis lymphomatosis

Egy ritka kórkép diagnosztikai nehézségei

Translated title of the contribution: Intravascular lymphomatosis: Diagnostic problems of a rare disease

Mónika Szóts, László Bors, E. Kálmán, L. Szapáry, Zsolt Illés

Research output: Contribution to journalArticle

Abstract

Intravascular lymphomatosis is a rare systemic disease characterized by proliferation of malignant B or rarely T lymphocytes. Skin and the brain are predominantly affected. We describe a patient presenting with focal neurological signs and progressive dementia. Cerebral neuroimaging findings were nonspecific. Postmortem examination revealed intravascular proliferation of atypical mononuclear cells in the lumens of small vessels in all organs. The authors conclude that diagnosis requires a high index of suspicion and pathological examination of the affected organs, but is rarely made ante mortem.

Original languageHungarian
Pages (from-to)749-752
Number of pages4
JournalOrvosi Hetilap
Volume148
Issue number16
DOIs
Publication statusPublished - Apr 22 2007

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Rare Diseases
Neuroimaging
Dementia
Autopsy
T-Lymphocytes
Skin
Brain

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Intravascularis lymphomatosis : Egy ritka kórkép diagnosztikai nehézségei. / Szóts, Mónika; Bors, László; Kálmán, E.; Szapáry, L.; Illés, Zsolt.

In: Orvosi Hetilap, Vol. 148, No. 16, 22.04.2007, p. 749-752.

Research output: Contribution to journalArticle

Szóts, Mónika ; Bors, László ; Kálmán, E. ; Szapáry, L. ; Illés, Zsolt. / Intravascularis lymphomatosis : Egy ritka kórkép diagnosztikai nehézségei. In: Orvosi Hetilap. 2007 ; Vol. 148, No. 16. pp. 749-752.
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