Felnottkori congenitalis szívsebészet gyermekkardioló giai és szívsebészeti központban

Translated title of the contribution: Grown-up congenital heart programme in a tertiary care pediatric cardiac centre

László Király, András Temesvári, Andrea Székely, Zsolt Prodán, Csilla Liptai, László Szudi, István Hartyánszky, Csilla Havrancsik, A. Szatmári

Research output: Contribution to journalArticle

1 Citation (Scopus)

Abstract

Introduction: Owing to excellent survival following primary repair over 80% of congenital cardiac patients reach adulthood, half of them requiring continuous specialist care and one-third needing further reoperation. The ample variety and complexity of lesions warrant individualised treatment strategy. Objective: This study focuses on grown-up congential heart (GUCH) programme in the settings of a tertiary pediatric cardiac centre. Methods: Patients underwent corrective surgical procedures in pediatric facilities (theatre, ICU, wards) with a close involvement of adult cardiology/anaesthetic team. Patients were divided into simple/complex groups. Results: Simple group of comprised patients (n = 20) having ASD-II (18/20) sinus venosus ASD (2/20) repair without morbidity/mortality from right subaxillary thoracotomy in 17/20. Complex group (n = 20): corrective surgery for tetralogy of Fallot (6), LVOT-aortic valve repairs (4), allograft conduit exchange (3), TCPC (3), miscellaneous procedures (4) were performed as reoperations in 16/20 at 16.1 ± 8.1 years following previous operations (median: 1.96, range 1-4). Postoperative right ventricle- (1), acute renal (1) failure and ARDS (1) fully recovered. One patient was lost for multi-organ-failure due to low cardiac output syndrome caused by chronic RV failure. Preoperative cyanosis was a risk factor for postoperative complications (p = 0.01). All survivors are symptom-free. No significant difference in ITU stay/LOS was observed between simple and complex groups. Conclusions: This study represents the initial experience of authors with GUCH. The number of GUCH patients is expected to rise with an upgrade shift in surgical complexity and severity requiring a multidisciplinary approach. It is advocated that complex GUCH cases should be performed by teams experienced in congenital reconstructive surgery. Patients following complex GUCH procedures have a comparable hospital course to patients undergoing simple cardiac operations.

Original languageHungarian
Pages (from-to)209-214
Number of pages6
JournalOrvosi Hetilap
Volume146
Issue number5
Publication statusPublished - 2005

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Tertiary Healthcare
Pediatrics
Reoperation
Reconstructive Surgical Procedures
Low Cardiac Output
Cyanosis
Tetralogy of Fallot
Thoracotomy
Cardiology
Aortic Valve
Acute Kidney Injury
Heart Ventricles
Allografts
Survivors
Anesthetics
Morbidity
Survival
Mortality

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Király, L., Temesvári, A., Székely, A., Prodán, Z., Liptai, C., Szudi, L., ... Szatmári, A. (2005). Felnottkori congenitalis szívsebészet gyermekkardioló giai és szívsebészeti központban. Orvosi Hetilap, 146(5), 209-214.

Felnottkori congenitalis szívsebészet gyermekkardioló giai és szívsebészeti központban. / Király, László; Temesvári, András; Székely, Andrea; Prodán, Zsolt; Liptai, Csilla; Szudi, László; Hartyánszky, István; Havrancsik, Csilla; Szatmári, A.

In: Orvosi Hetilap, Vol. 146, No. 5, 2005, p. 209-214.

Research output: Contribution to journalArticle

Király, L, Temesvári, A, Székely, A, Prodán, Z, Liptai, C, Szudi, L, Hartyánszky, I, Havrancsik, C & Szatmári, A 2005, 'Felnottkori congenitalis szívsebészet gyermekkardioló giai és szívsebészeti központban', Orvosi Hetilap, vol. 146, no. 5, pp. 209-214.
Király L, Temesvári A, Székely A, Prodán Z, Liptai C, Szudi L et al. Felnottkori congenitalis szívsebészet gyermekkardioló giai és szívsebészeti központban. Orvosi Hetilap. 2005;146(5):209-214.
Király, László ; Temesvári, András ; Székely, Andrea ; Prodán, Zsolt ; Liptai, Csilla ; Szudi, László ; Hartyánszky, István ; Havrancsik, Csilla ; Szatmári, A. / Felnottkori congenitalis szívsebészet gyermekkardioló giai és szívsebészeti központban. In: Orvosi Hetilap. 2005 ; Vol. 146, No. 5. pp. 209-214.
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AU - Temesvári, András

AU - Székely, Andrea

AU - Prodán, Zsolt

AU - Liptai, Csilla

AU - Szudi, László

AU - Hartyánszky, István

AU - Havrancsik, Csilla

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