Ebstein-anomália--a felnottkorban végzett mutétekkel kapcsolatos tapasztalatok.

Translated title of the contribution: Ebstein's anomaly--experiences with surgical treatment in adulthood

István Szentkirályi, Zoltán Galajda, Endre Jagamos, C. Papp, Ferenc Bodnár, Tibor Fülöp, Arpád Péterffy

Research output: Contribution to journalArticle

Abstract

INTRODUCTION: Long time results with operative treatment of Ebstein anomaly were examined. PATIENTS AND METHODS: From January 1985 to March 2001 16 patients with Ebstein anomaly were operated on. Ages ranged from 16 to 49 years at the time of operation. In 7 cases tricuspid valve repair was possible, and in 9 cases prosthetic valve was inserted. In all but one biological prosthesis has been used. In 15 cases atrial septal defect occurred as a concomitant anomaly, which was closed by direct suture in 9 cases and with patch (2 Dacron, 4 pericardium) in 6 cases. RESULTS: There was no early death (30 days postoperatively). 1 patient following tricuspid repair was reoperated on at the 9th postoperative day because of significant tricuspid insufficiency. Tricuspid valve replacement was performed with a biological prostheses. There were 3 late deaths: 2 patients (12.5%) in the first postoperative year (1 cardiac cause, 1 unknown), 1 patient died 6 years postoperatively following reoperation. There were 3 more patients requiring reoperation (total reoperation rate 28.6%) one of them a few days after the primary operation and two others 9 and 11 years following the first operation. 13 patients were recalled to control investigations. The authors could not contact 2 patients, 1 patient living abroad could not appear at our clinic. 10 patients have been investigated 6 months to 16 years after the operation. There were 9 patients in New York Heart Association class I or II. 2 patients had their own repaired valve; both had tricuspid insufficiency grade III. Both were completely active. 8 patients had previously tricuspid valve replacement and good valve function, but six of them have not been working any more. There were 5 female patients under 35 at the time of operation and 2 of them had successful pregnancies. CONCLUSIONS: Patients with Ebstein anomaly in NYHA stage III-IV. can be successfully treated surgically.

Original languageHungarian
Pages (from-to)2289-2292
Number of pages4
JournalOrvosi Hetilap
Volume145
Issue number45
Publication statusPublished - Nov 7 2004

Fingerprint

Ebstein Anomaly
Therapeutics
Tricuspid Valve
Reoperation
Prostheses and Implants
Polyethylene Terephthalates
Atrial Heart Septal Defects
Pericardium

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Szentkirályi, I., Galajda, Z., Jagamos, E., Papp, C., Bodnár, F., Fülöp, T., & Péterffy, A. (2004). Ebstein-anomália--a felnottkorban végzett mutétekkel kapcsolatos tapasztalatok. Orvosi Hetilap, 145(45), 2289-2292.

Ebstein-anomália--a felnottkorban végzett mutétekkel kapcsolatos tapasztalatok. / Szentkirályi, István; Galajda, Zoltán; Jagamos, Endre; Papp, C.; Bodnár, Ferenc; Fülöp, Tibor; Péterffy, Arpád.

In: Orvosi Hetilap, Vol. 145, No. 45, 07.11.2004, p. 2289-2292.

Research output: Contribution to journalArticle

Szentkirályi, I, Galajda, Z, Jagamos, E, Papp, C, Bodnár, F, Fülöp, T & Péterffy, A 2004, 'Ebstein-anomália--a felnottkorban végzett mutétekkel kapcsolatos tapasztalatok.', Orvosi Hetilap, vol. 145, no. 45, pp. 2289-2292.
Szentkirályi I, Galajda Z, Jagamos E, Papp C, Bodnár F, Fülöp T et al. Ebstein-anomália--a felnottkorban végzett mutétekkel kapcsolatos tapasztalatok. Orvosi Hetilap. 2004 Nov 7;145(45):2289-2292.
Szentkirályi, István ; Galajda, Zoltán ; Jagamos, Endre ; Papp, C. ; Bodnár, Ferenc ; Fülöp, Tibor ; Péterffy, Arpád. / Ebstein-anomália--a felnottkorban végzett mutétekkel kapcsolatos tapasztalatok. In: Orvosi Hetilap. 2004 ; Vol. 145, No. 45. pp. 2289-2292.
@article{a3ffbd55baba48cda76175f5cb4fe52e,
title = "Ebstein-anom{\'a}lia--a felnottkorban v{\'e}gzett mut{\'e}tekkel kapcsolatos tapasztalatok.",
abstract = "INTRODUCTION: Long time results with operative treatment of Ebstein anomaly were examined. PATIENTS AND METHODS: From January 1985 to March 2001 16 patients with Ebstein anomaly were operated on. Ages ranged from 16 to 49 years at the time of operation. In 7 cases tricuspid valve repair was possible, and in 9 cases prosthetic valve was inserted. In all but one biological prosthesis has been used. In 15 cases atrial septal defect occurred as a concomitant anomaly, which was closed by direct suture in 9 cases and with patch (2 Dacron, 4 pericardium) in 6 cases. RESULTS: There was no early death (30 days postoperatively). 1 patient following tricuspid repair was reoperated on at the 9th postoperative day because of significant tricuspid insufficiency. Tricuspid valve replacement was performed with a biological prostheses. There were 3 late deaths: 2 patients (12.5{\%}) in the first postoperative year (1 cardiac cause, 1 unknown), 1 patient died 6 years postoperatively following reoperation. There were 3 more patients requiring reoperation (total reoperation rate 28.6{\%}) one of them a few days after the primary operation and two others 9 and 11 years following the first operation. 13 patients were recalled to control investigations. The authors could not contact 2 patients, 1 patient living abroad could not appear at our clinic. 10 patients have been investigated 6 months to 16 years after the operation. There were 9 patients in New York Heart Association class I or II. 2 patients had their own repaired valve; both had tricuspid insufficiency grade III. Both were completely active. 8 patients had previously tricuspid valve replacement and good valve function, but six of them have not been working any more. There were 5 female patients under 35 at the time of operation and 2 of them had successful pregnancies. CONCLUSIONS: Patients with Ebstein anomaly in NYHA stage III-IV. can be successfully treated surgically.",
author = "Istv{\'a}n Szentkir{\'a}lyi and Zolt{\'a}n Galajda and Endre Jagamos and C. Papp and Ferenc Bodn{\'a}r and Tibor F{\"u}l{\"o}p and Arp{\'a}d P{\'e}terffy",
year = "2004",
month = "11",
day = "7",
language = "Hungarian",
volume = "145",
pages = "2289--2292",
journal = "Orvosi Hetilap",
issn = "0030-6002",
publisher = "Akademiai Kiado",
number = "45",

}

TY - JOUR

T1 - Ebstein-anomália--a felnottkorban végzett mutétekkel kapcsolatos tapasztalatok.

AU - Szentkirályi, István

AU - Galajda, Zoltán

AU - Jagamos, Endre

AU - Papp, C.

AU - Bodnár, Ferenc

AU - Fülöp, Tibor

AU - Péterffy, Arpád

PY - 2004/11/7

Y1 - 2004/11/7

N2 - INTRODUCTION: Long time results with operative treatment of Ebstein anomaly were examined. PATIENTS AND METHODS: From January 1985 to March 2001 16 patients with Ebstein anomaly were operated on. Ages ranged from 16 to 49 years at the time of operation. In 7 cases tricuspid valve repair was possible, and in 9 cases prosthetic valve was inserted. In all but one biological prosthesis has been used. In 15 cases atrial septal defect occurred as a concomitant anomaly, which was closed by direct suture in 9 cases and with patch (2 Dacron, 4 pericardium) in 6 cases. RESULTS: There was no early death (30 days postoperatively). 1 patient following tricuspid repair was reoperated on at the 9th postoperative day because of significant tricuspid insufficiency. Tricuspid valve replacement was performed with a biological prostheses. There were 3 late deaths: 2 patients (12.5%) in the first postoperative year (1 cardiac cause, 1 unknown), 1 patient died 6 years postoperatively following reoperation. There were 3 more patients requiring reoperation (total reoperation rate 28.6%) one of them a few days after the primary operation and two others 9 and 11 years following the first operation. 13 patients were recalled to control investigations. The authors could not contact 2 patients, 1 patient living abroad could not appear at our clinic. 10 patients have been investigated 6 months to 16 years after the operation. There were 9 patients in New York Heart Association class I or II. 2 patients had their own repaired valve; both had tricuspid insufficiency grade III. Both were completely active. 8 patients had previously tricuspid valve replacement and good valve function, but six of them have not been working any more. There were 5 female patients under 35 at the time of operation and 2 of them had successful pregnancies. CONCLUSIONS: Patients with Ebstein anomaly in NYHA stage III-IV. can be successfully treated surgically.

AB - INTRODUCTION: Long time results with operative treatment of Ebstein anomaly were examined. PATIENTS AND METHODS: From January 1985 to March 2001 16 patients with Ebstein anomaly were operated on. Ages ranged from 16 to 49 years at the time of operation. In 7 cases tricuspid valve repair was possible, and in 9 cases prosthetic valve was inserted. In all but one biological prosthesis has been used. In 15 cases atrial septal defect occurred as a concomitant anomaly, which was closed by direct suture in 9 cases and with patch (2 Dacron, 4 pericardium) in 6 cases. RESULTS: There was no early death (30 days postoperatively). 1 patient following tricuspid repair was reoperated on at the 9th postoperative day because of significant tricuspid insufficiency. Tricuspid valve replacement was performed with a biological prostheses. There were 3 late deaths: 2 patients (12.5%) in the first postoperative year (1 cardiac cause, 1 unknown), 1 patient died 6 years postoperatively following reoperation. There were 3 more patients requiring reoperation (total reoperation rate 28.6%) one of them a few days after the primary operation and two others 9 and 11 years following the first operation. 13 patients were recalled to control investigations. The authors could not contact 2 patients, 1 patient living abroad could not appear at our clinic. 10 patients have been investigated 6 months to 16 years after the operation. There were 9 patients in New York Heart Association class I or II. 2 patients had their own repaired valve; both had tricuspid insufficiency grade III. Both were completely active. 8 patients had previously tricuspid valve replacement and good valve function, but six of them have not been working any more. There were 5 female patients under 35 at the time of operation and 2 of them had successful pregnancies. CONCLUSIONS: Patients with Ebstein anomaly in NYHA stage III-IV. can be successfully treated surgically.

UR - http://www.scopus.com/inward/record.url?scp=16544389342&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=16544389342&partnerID=8YFLogxK

M3 - Article

C2 - 15573893

AN - SCOPUS:16544389342

VL - 145

SP - 2289

EP - 2292

JO - Orvosi Hetilap

JF - Orvosi Hetilap

SN - 0030-6002

IS - 45

ER -