In a 17 year old boy presenting with abdominal pain, fever and failure to thrive the clinical diagnosis was Crohn's disease. He died from postoperative complications after hemicolectomy. The autopsy revealed ganglioneuromatosis of the intestines, a disorder which occurs in multiple endocrine neoplasia type IIb. Better awareness of this syndrome could result in an earlier diagnosis which could help therapy and improve the prognosis.
|Number of pages||4|
|Journal||Children's Hospital Quarterly|
|Publication status||Published - Dec 1 1992|
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health