Cochlear implantation in osteogenesis imperfecta

J. Szilvássy, J. Jóri, J. Czigner, F. Tóth, Z. Szilvássy, J. G. Kiss

Research output: Contribution to journalArticle

13 Citations (Scopus)


Cochlear implantation in osteogenesis imperfecta. A case is reported in which a Nucleus 22 channel intracochlear implant was applied to a Hungarian woman (age 50 yr) with profound deafness associated with osteogenesis imperfecta. Successful intracochlear insertion of the 22 electrodes resulted in a 70 dB hearing improvement at frequencies 250-2000 HZ. Nevertheless, a characteristic facial twitching appeared upon activation of electrodes 9-13. Inactivation of these electrodes abolished the non-acoustic nerve excitation with preservation of acoustic performance. Osteogenesis imperfecta may involve a state of risk for non-acoustic nerve activation in cochlear implant patients possibly resulting from a reduced impedance to current spread by abnormal bone tissue. This, however can be overcome by simple programming manoeuvres.

Original languageEnglish
Pages (from-to)253-256
Number of pages4
JournalActa Oto-Rhino-Laryngologica Belgica
Issue number3
Publication statusPublished - Dec 1 1998


  • Cochlear implantation
  • Field stimulation
  • Osteogenesis imperfecta

ASJC Scopus subject areas

  • Otorhinolaryngology

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