Egy ritkán felismert ritka betegség: A Behcet-kór

Translated title of the contribution: Behcet's disease: A hardly diagnosed orphan disorder

E. Kiss, Judit Dohán, J. Németh, G. Poór

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

Behcet's disease is a multisystem autoimmune disease with variable clinial manifestations. The diagnosis may pose a difficult challenge for the clinician, who has to be familiar with the wide spectrum and combination of the symptoms of Behcet's disease. It is considered a rare disease in Hungary, and there are only few reports on Behcet's disease in the Hungarian literature. However, the past history of Hungary, the worldwide growing incidence of the disease, and the authors' experience raise the possibility that the occurrence of the disease is higher than previously thought. In this review the authors present and discuss literature data on the pathogenesis and pathomechanism, as well as their own experience concerning the symptomatology of Behcet's disease in order to promote diagnosis and offer adequate therapy for the patients. The authors presume that the importance of the disease is underestimated in Hungary due to a considerable number of unrecognized cases and they propose to establish a national registry for Behcets disease.

Original languageHungarian
Pages (from-to)93-101
Number of pages9
JournalOrvosi Hetilap
Volume154
Issue number3
DOIs
Publication statusPublished - Jan 1 2013

Fingerprint

Orphaned Children
Behcet Syndrome
Hungary
Rare Diseases
Autoimmune Diseases
Registries
History
Incidence

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Egy ritkán felismert ritka betegség : A Behcet-kór. / Kiss, E.; Dohán, Judit; Németh, J.; Poór, G.

In: Orvosi Hetilap, Vol. 154, No. 3, 01.01.2013, p. 93-101.

Research output: Contribution to journalArticle

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