Arrhythmogen jobb kamrai dysplasia. Esetismertetés és irodalmi áttekintés.

Translated title of the contribution: Arrhythmogenic right ventricular dysplasia. Case report and review of the literature

I. Kolonics, M. György, M. Lengyel, L. Hegyi

Research output: Contribution to journalArticle

1 Citation (Scopus)

Abstract

Two cases of arrhythmogenic right ventricular dysplasia are described. The most important clinical features of the disease are malignant ventricular arrhythmia and sudden death. It is characterized by the loss of right ventricular musculature and by the fatty and connective tissue infiltration of the right ventricular wall. The diagnosis is based on the typical echocardiographic appearance of right ventricular dilatation, on the presence of negative T waves in leads V1-4 on the resting ECG and on ventricular tachycardia of left bundle branch block pattern. Right heart failure develops only in the late phase of the disease. Genetic defect might be an etiologic factor. In conclusion authors suggest that in case of left bundle branch block ventricular tachycardia or Adams-Stokes syndrome in young adults echocardiography and family screening are necessary.

Original languageHungarian
Pages (from-to)2807-2811
Number of pages5
JournalOrvosi Hetilap
Volume134
Issue number51
Publication statusPublished - Dec 19 1993

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Arrhythmogenic Right Ventricular Dysplasia
Bundle-Branch Block
Ventricular Tachycardia
Adams-Stokes Syndrome
Sudden Death
Connective Tissue
Echocardiography
Adipose Tissue
Cardiac Arrhythmias
Dilatation
Young Adult
Electrocardiography
Heart Failure

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Kolonics, I., György, M., Lengyel, M., & Hegyi, L. (1993). Arrhythmogen jobb kamrai dysplasia. Esetismertetés és irodalmi áttekintés. Orvosi Hetilap, 134(51), 2807-2811.

Arrhythmogen jobb kamrai dysplasia. Esetismertetés és irodalmi áttekintés. / Kolonics, I.; György, M.; Lengyel, M.; Hegyi, L.

In: Orvosi Hetilap, Vol. 134, No. 51, 19.12.1993, p. 2807-2811.

Research output: Contribution to journalArticle

Kolonics, I, György, M, Lengyel, M & Hegyi, L 1993, 'Arrhythmogen jobb kamrai dysplasia. Esetismertetés és irodalmi áttekintés.', Orvosi Hetilap, vol. 134, no. 51, pp. 2807-2811.
Kolonics, I. ; György, M. ; Lengyel, M. ; Hegyi, L. / Arrhythmogen jobb kamrai dysplasia. Esetismertetés és irodalmi áttekintés. In: Orvosi Hetilap. 1993 ; Vol. 134, No. 51. pp. 2807-2811.
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