A rare form of adrenal Cushing's syndrome

Gábor Sohár, Nikolette Szücs, Károly Rácz, Béla Merkely, Kálmán Hüttl, Pál Sármán, Andrea Györkös, Beáta Gasztonyi

Research output: Contribution to journalArticle


The authors present the case history of a 74-year-old male suffering from aortic coarctation. His endocrine evaluation was initiated because of severe hypokalemia. The diagnostic procedures revealed the presence of Cushing's syndrome caused by bilateral macronodular adrenal hyperplasia. Because of the high risk of surgical treatment due to his cardiac condition, the patient was treated with the steroid biosynthesis inhibitor ketoconazole, which resulted in a clinical and biochemical regression of hypercortisolism. After interventional treatment of the aortic coarctation the physical and cardiac condition of the patient showed a significant improvement, indicating that despite an old age, surgery offered a valuable tool for management of the disease. To the best knowledge of the authors, the coexistence of aortic coarctation and bilateral macronodular adrenal hyperplasia has not been previously reported. Orv. Hetil., 154(50), 1999-2002.

Original languageEnglish
Pages (from-to)1999-2002
Number of pages4
JournalOrvosi hetilap
Issue number50
Publication statusPublished - Dec 1 2013



  • Aortic coarctation
  • Bilateral macronodular adrenal hyperplasia
  • Cushing's syndrome
  • Cushing-szindróma

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Sohár, G., Szücs, N., Rácz, K., Merkely, B., Hüttl, K., Sármán, P., Györkös, A., & Gasztonyi, B. (2013). A rare form of adrenal Cushing's syndrome. Orvosi hetilap, 154(50), 1999-2002. https://doi.org/10.1556/OH.2013.29779